@article{ author = {Ebrahimi, H.A. and Shams-Al-Dini, S.}, title = {ATAXIA - TELANGIECTASIA: REPORT OF 2 CASES}, abstract ={The ataxia - telangiectasia or Louis - Bar syndrome is a rare hereditary disease. The inheritance pattern is autosomal recessive, locus gene has been mapped to the long arm of chromosome 11. The onset of the disease coincides more or less with the acquisition of walking, which is awkward and unsteady. The characteristic telangiectatic lesions, are mainly subpapillary vascular plexuses of the bulbar conjunctivae and over the ears. In these cases ataxia at 1.5 and 2 years old appeared , but telangiectatic lesions appeared at 4 years. There are high circulating levels of alpha - fetoprotein this is thought to be due to immaturity of the liver, and serum concentration of IgA and IgG are reduced. In these cases (one brother and sister), serum alpha fetoprotein significantly increased. In the sister, IgA is absent and in the brother level of IgA is decreased.}, Keywords = {1) Ataxia - telangiectasia 2) Louis - Bar syndrome 3) Telangiectasia}, volume = {2}, Number = {0}, pages = {225-230}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1857-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1857-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Khatami, D. and Taghipor, S. and Daneshmand, M.A. and Khalajzadeh, M.R.}, title = {PRIMARY IMMUNOBLASTIC LYMPHOMA OF OVARY: A CASE REPORT}, abstract ={A 55 - years - old woman was referred to Firoozabadi General Hospital with abdominal pain and vomiting of 2 months duration. Physical examination revealed a pelvic mass located in left lower quadrant, and no any lymph node enlargement was noted. At laparatomy a large solid mass was removed, with irregular surface and necrotic areas. Pathology was reported as primary diffuse large cell immunoblastic lymphoma of the ovary. Diagnosis was also confirmed by immunohistochemical studies. Review of literature from 1990 -95 revealed only two cases with this diagnosis , and in Imam Khomeini Cancer Institute reports there were two such cases during last 20 years.}, Keywords = {1) Ovarian tumor 2) Pelvic mass 3) Immunoblastic lymphoma}, volume = {2}, Number = {0}, pages = {231-234}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1858-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1858-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Roodpeyma, S. and Babaei, H.A. and Vallaei, N.}, title = {STREPTOCOCCAL PHARYNGITIS IN CHILDREN: SURVEY OF 100 CASES}, abstract ={This prospective study was designed to find the incidence of streptococcal pharyngitis in childhood sore throat and also to compare the clinical diagnosis of disease with the results of throat cultures. Children, 5 to 15 years of age with sore throat who were seen in pediatric out - patients department formed the subjects of this study. The duration of study was one year (October 1992 - October 1993). There were 443 children with sore throat. 100 patients (22.5%) had positive throat culture (group A Beta hemolytic streptococci) . 53 patients (53%) were male and 47% were female. The mean age of the group was 8.8 ± 3 years. Clinical findings in order of frequency were as follow: redness of pharynx 99% , acute onset of symptoms 86% , fever 84% 1 exudate on tonsils 69% , enlargement and tenderness of anterior cervical lymph nodes 30% , and associated gastrointestinal symptoms 22% . Seasonal prevalence of disease were as follow: spring 35%, winter 34% , autumn 28 % and summer 3%. 53% of this patients had 5 clinical symptoms. 5 clinical findings such as sore throat + fever + acute onset of disease + redness of pharynx + exudate on tonsils and absence of viral symptoms (cough, coryza, conjunctivitis, hoarseness) had a sensitivity of 57% , specititv of 98% J positive predictive value of 89% , negative predictive value of 89% and efficiency of 89%. This study showed that in the absence of laboratory facilities careful clinical findings can be helpful for reaching accurate diagnosis of streptococcal pharyngitis.}, Keywords = {1) Streptococcal pharyngitis 2) Throat culture 3) Sore throat}, volume = {2}, Number = {0}, pages = {235-242}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1859-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1859-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Samaee, H.}, title = {THE INCIDENCE AND FREQUENCY OF SIGNS & SYMPTOMS AND PROGNOSIS OF POLYCYTHEMIA IN NEWBORNS}, abstract ={In order to evaluate the incidence and frequency of clinical and laboratory findings in newborns with polycythemia in Tehran a retrospective study was carried out in newborns who were admitted in newborn service in Ali Asghar Children Hospital between years 1988-1995 . During this period 3086 newborns were admitted and 32 patients had central hematocrit above 65% (1.03%) . Of the polycythemic infants, 84.4 % were sympthomatic. Frequent signs and symptoms included: cyanosis 28. 1 %, plethora 28.1%, jitteriness 25%, poor feeding 25%, lethargia 21.8%, respiratory distress 12.5% and hypotonia 12.5% . Other findings included hypoglycemia 43.7% and hyperbilirubinemia 25% . Of the polycythemic infants, 15.6% had no clinical or laboratory abnormality. It was noted that SGA & LGA newborns are more prone to polycythemia. With early diagnosis and appropriate treatment the prognosis is excellent.}, Keywords = {1) Polycythemia 2) Hypoglycemia 3) Hyperviscosity 4) Premature baby}, volume = {2}, Number = {0}, pages = {243-247}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1860-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1860-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {ArabMohammadHosseini, A.}, title = {CLINICAL , LABORATORY FINDINGS AND PROGNOSIS OF NEONATAL SEPSIS: SURVEY OF 100 CASES}, abstract ={In order to evaluate the frequency of clinical and laboratory findings of neonatal sepsis in Tehran, a retrospective study was carried out in 100 newborns who were admittedin newborn service of Ali Asghar Children Hospital with diagnosis of neonatal sepsis and eventually had positive blood cultures. 56% of this patients were above 1 week of age (late neonatal sepsis) and 44% were below 1 week (early neonatal sepsis). Among infected newborns, 67% were male and 33% were female. The frequency of clinical findings was: decreased reflexes (74%), poor feeding 44% , lethargy 34%, Jaundice 31%, hypothermia 25%, respiratory distress 24% J vomiting 19%, cyanosis 18% , hyperthermia 18% and irritability 17%. Other findings included: Leukopenia 22% , increased band cells 28% , thrombocytopenia 36%, prolonged PIT 26% and PT 20% . With early diagnosis and treatment 82% of the patients recovered completely.}, Keywords = {1) Sepsis 2) Leukopenia 3) Early neonatal sepsis 4) Late neonatal sepsis}, volume = {2}, Number = {0}, pages = {248-253}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1861-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1861-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Ghoraian, M.A. and Moshgou, M. and Sarami, A.}, title = {ESOPHAGEAL CARCINOMA: SURVEY OF 92 CASES}, abstract ={The study was conducted to determine the manifestation of esophageal carcinoma in Iranian patients. 92 cases with esophageal carcinoma that hospitalized in Rasool - E Akram and Rahnamoon General Hospitals were studied retrospectively. 57% of the patients were males and 62% in 50 - 70 years old ages. The common symptoms were: dysphagia (96%), odynophagia (69%) , restrosternal pain (59%) , regurgitation (53%) , nausea and vomiting (47%), coughing (17%) and hematemesis (8%). The common clinical signs were: cachexia (62%) , lymphadenopathy (16.5%) , hoarseness (9%) and hepatomegaly (7.6%) . 69% of the tumors were detected in distal third of the esophagus and cardia. Squamous cell carcinoma (S.C.C) was the most common pathologic diagnosis. The post operative staging of the tumors were: stage I (22%) s stage 1/(15%) , stage 11/(49%) and stage IV(15%). The mortality rate of this patients was 7% . In conclusion, a significant percent of the patients were detected in early stages and were successfully managed. Many of these patients had no major problem in follow - up.}, Keywords = {1) Esophageal carcinoma 2) Dysphagia 3) Squamous cell carcinoma (S.C.C)}, volume = {2}, Number = {0}, pages = {254-260}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1862-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1862-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Homayounfar, H.}, title = {RECENT ADVANCES REGARDING PLATELETS}, abstract ={Platelets as cellular elements are the constituants of blood tissue and their main function is to participate in hemostatic processes. The glycocalyx which intimately surrounds the platelets contains a number of glycoproteins which are responsible for blood group specificity (ABO), tissue compatibility (human leukocyte antigen = HLA) , and platelet antigenicity. Platelets contain granules which are involved in many sorts of activities like maintaining the integrity of vascular endothelial cells. This process is mostly mediated by platelet derived growth factor (PDGF) Adhesion of platelets to each other and thrombus formation are mediated by different factors such as platelet activation and release of ADP which facilitate formation of glycoprotein and phospholipoprotein complexes in the membrane of neighboring platelets. TXA2 released from arachidonic acid originally from membrane otiosphotipides also plays a role in thrombus formation. Thrombus then binds to collagene fibers of subendothelium through VWF or fibronectins and prevents bleeding by forming platelets plugs. Platelets release factors such as I, V, VII to facilitate coagulation, and for this reason, are called thrombocytes. They also release heparin neutralizing proteins (PF4, TG) that help from clots at the injured sites. Finally, they participate in clot retraction through contractile proteines, specifically thrombostenin.}, Keywords = {1) Platelet 2) Hemostasis 3) Thrombus 4) Granule}, volume = {2}, Number = {0}, pages = {261-269}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1863-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1863-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Hoormazdi, M.}, title = {MULTIPLE LYMPHOMATOUS POLYPOSIS OF THE GASTROINTESTINAL TRACT: A CASE REPORT AND REVIEW OF THE LITERATURE}, abstract ={Multiple lymphomatous polyposis (M L P) is a rare type of gastrointestinal lymphoma presenting as multiple polyps involving large segments of the bowel. The lesions have been classified by immuno ­histochemical methods as • Mantle Zone Lymphoma' . According to our knowledge, no case of M L P has been reported in Iran. The 29 years old male who presented in this paper, is the youngest patient that has been reported in medical literature.}, Keywords = {1) Extranodal lymphome 2) Multiple lymphomatous polyposis (MLP) 3) Primary gastrointestinal lymphome}, volume = {2}, Number = {0}, pages = {270-275}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1864-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1864-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Hoomand, A. and Latifi, N.A.}, title = {SUPERIOR MESENTERIC ARTERY SYNDROME IN BURN INJURY: A CASE REPORT}, abstract ={Weight loss resulting from the hypermetabolic response to burn injury is not unusual and is often unavoidable. The loss of retroperitoneal fat has been postulated as a major factor in the cause of the uncommon complication of superior mesenteric artery syndrome. This syndrome is frequently treated nonoperatively with aggressive nutrition support. Nasojejunal feeding past the point of obstruction should be considered as the primary method of nutrition support. Alternatively, total parenteral nutrition or a combination of enteral and parenteral feeding may be necessary to meet nutritional needs until the duodenal obstruction resolves. This case study described the nutrition management of a burn patient who developed superior mesenteric artery syndrome.}, Keywords = {1) Burn injury 2) Weight loss 3) Nasojejunal feeding}, volume = {2}, Number = {0}, pages = {276-282}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1865-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1865-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1996} } @article{ author = {Amini, S.A. and Haghighi, L.}, title = {SPONTANEOUS HEMATOMA OF RECTUS SHEATH DURING PREGNANCY,A CASE REPORT}, abstract ={Rectus sheath hematoma can be an unusual cause of abdominal mass that may present as an acute intra - abdominal problem. There are multiple causes and 1 with a tnrouqt: history, usually some precipitating factor can be identified. Hematoma is frequently due to rupture of Epigastric vesseles and only rarely to rupture of Rectus Abdominis muscle fibers. Misdiagnosis may result in the performance of unnecessary surgical procedures. Ultrasound examination, CT scan, and magnetic resonance imaging (MRI) are useful in making an accurate diagnosis. Treatment is usually conservstive.ln this paper, a case of spontaneous Rectus sheath hematoma during pregnancy is reported.}, Keywords = {1) Hematoma 2) Abdominal wall 3) Muscles 4) Pregnancy}, volume = {2}, Number = {0}, pages = {97-101}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1866-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1866-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Jalali, S.A.}, title = {WOUND COMPLICATIONS FOLLOWING MASTECTOMY}, abstract ={Carcinoma of the breast is considered to be the number one cause of death for women in many countries. Diversity of opinion and contraversies still exist among specialists in taking a unified treatment protocol in this disease. Although in the present century, many researchers and specialists have been doing extensive work on this problem which has resulted in a large volume of written material on carcinoma of the breast, very little research has been done on perioperative complications of mastectomy. In this article we will show that the incidence of wound infection after mastectomy is very high and is many times greater than clean surgical cases, and even higher than clean - contaminated cases llkesuppuretive append icitis, In this study we performed a retrospective 12 year, review on wound complications of modified radical mastectomies (MRM) on 105 cases. Although these complication rates were high, they were comparable with those of international literature. This study also compares the rate of wound infection in MRM which is a clean surgical wound with the same number of suppurative appendicitis which were also retrospectively studied in a two - year - period and proved statistically that the rate of infection in MRM is higher than that of suppurative appendectomies, which is a clean-contaminated wound. In conclusion, factors which were thought to contribute to high rate of infection in a clean operation like that of MRM are discussed and preventive measure suggested.  }, Keywords = {1) Mastectomy 2) Infection 3) Carcinoma of thebreast}, volume = {2}, Number = {0}, pages = {102-115}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1867-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1867-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Haghighi, L.}, title = {NEW METHODS IN FETAL SURGERY}, abstract ={The field of prenatal diagnosis of congenital anomalies has had great advances in recent years. Today we are able to diagnose different fetal anomalies in early developmental stages, and correct some of them, through prenatal fetal surgery. In this paper, we begin by describing the advances in surgical treatment of some fetal diseases such as, diaphragmatic hernia, lung sequestration, pleural effusion, congenital cystic adenomatoid malformation (CCAM) urinary tract obstructions , sacrococcygeal teratoma and twin-twin transfusion syndrome, then discuss new fields of research generated by the study of fetal surgery.}, Keywords = {1) Fetal Surgery 2) Fetal malformation 3) Diaphragmatic hernia}, volume = {2}, Number = {0}, pages = {116-121}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1868-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1868-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Ataipour, Y. and Aris, S. and Ghorbani, G. and Ghods, A.}, title = {PREVALENCE OF IgA NEPHROPATHY IN PATIENTS WITH IDIOPATHIC GLOMERULONEPHRITIS}, abstract ={During a 14-month period (Dec. 1990-Jan. 1992) , renal biopsies were performed on 105 patients with suspected glomerular disease. All specimens were processed for light microscopy (L.M) and immunoflourescence. Work-up revealed 21 patients to suffer a systemic glomerular disease and glomerular disease was found to be primery in 85 cases. Predominant IgG deposition was noted in 71 cases with primary glomerular disease and IgA deposition was predominant in 13 cases (15.5%) . Among patients with IgA nephropathy there were 11 males and 2 females, with a mean age of 31 ± 8.3 years (range 18-48). All except one were normotensive . There was neptuotic range proteinuria in 5 and elevated serum IgA in 9 cases. 24-hour proteinuria was significantly lower among those with IgA nephropathy(3 ± 2.03 g/day vs. 5.87 ± 0.45 g/day, p<0.01). Serum 'lgA was significantly higher among patients with IgA nephropathy(447.4 ± 177 mg/dl vs. 252 ± 118.6 mg/dl, p<0.001). There was only one cases of hypocamplementemia (C3A9 mgldl). We found FSGN to be the most common pathology reported on LM for those with IgA nephropathy. We concludethatlgA nephropathy is ranther common in our population (15.5% of primary glomerular disease), the prevalence being lower than the Asia-Pacific region, while higher than that reported for North America}, Keywords = {1) IgA Nephropathy 2) Primary glomerulonephritis 3) Immune Complex 4) FSGN }, volume = {2}, Number = {0}, pages = {122-126}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1869-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1869-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Farhadi, M. and Moshrefi, M.}, title = {FUNCTIONAL ENDOSCOPIC SINUS SURGERY REPORT OF 200 CASES}, abstract ={The application of functional endoscopic sinus surgery (FESS) for treatment of chronic paranasal sinus diseases had become widely accepted. The diagnostic and therapeutic potential provided by transnasal endoscopic approach has allowed us to manage a variety of disorders other than inffammatory diseases of the nasal cavity and paranasal sinuses. In this prospective study indications, complications and results of FESS in 200 patients is reported. The pathologic conditions that necessitated surgical intervention were: chronic sinusitis with or without polyposis (88.5 %), antrochoanal polyp(2.97%), inverting papifoma(1.78 %), hemangioma(1.19 %) and meucocele of maxillary sinus (0.59 %). The operative metod was mainly based upon the Messer klinger technique. Major complications occurred only in %59 namely postoperative hemorrhage which was easily controlled. Minor complications occured in 8% of cases that include, periorbital hematoma (1.19 %) r obstruction of the maxillary sinus ostium (1.78%), and synechia between middle turbinate and lateral nasal wall (5.16 %) s which were almost entirely repaired during the post operative follow up. 6-24 month follow ups of our patients revealed a total recovery of rate of 95.88 %, which is comparable to the results of FESS in well know centers through the world .}, Keywords = {1) Endoscopic surgery 2) Paranasal sinus 3) FESS}, volume = {2}, Number = {0}, pages = {127-138}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1870-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1870-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Modaghegh, B.}, title = {OSTEOBLASTOMA OF 3 ADJACENT VERTEBRAE WITH COMOLETE SPASTIC PARAPLEGIA AND SCOLIOSIS,A CASE REPORT}, abstract ={A thirteen years old girl was referred for back pain and right thoracic scoliosis, complete spastic paraplegia, bladder and bowel incontinence . The patient had history of back pain for a 4 year period eventually leading to scoliosis and neurological deficiency. Symptoms gradually worsened up to 4 months before admission converting to complete spastic paraplegia and bladder and bowel incontinence . Imaging study revealed destruction of T7, T8J T9 vertebral bodies with severe cord compression. Resection of tumor and cord decompression plus anterior spinal fusion were performed by two rib strut graft. uneventful neurologic recovery followed surgery and then the patient underwent posterior spinal fusion and compression and distraction Harrington rod instrumentation for structural scoliosis. A 4 year period toltow-up revealed full recovery and solid spinal fusion and she is now walking without aid of any devices. The histologic study of pathologic bone tissue revealed osteoblastoma. Review of literatures confirmed no previous report on affection of three adjacent vertebral bodies by osteoblastoma.}, Keywords = {1) Osteoblastoma 2) Vertebrae 3) Scoliosis 4) Paraplegia}, volume = {2}, Number = {0}, pages = {139-144}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1871-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1871-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Malakouti, K. and Norouzi, F. and Tadayon, S.}, title = {RELATIONSHIP BETWEEN TYPE A AND B PERSONALITY WITH ACADEMIC ACHIEVEMENT}, abstract ={The primary aim of this study was to investigate the variance in academic achievement in two personality types, namely A and B. 100 medical students at internship level from Zahedan University of Medical Sciences were dissociated on the basis of type A and B by type A behavior questioner . In addition, intensity of anxiety and the experience of a recent stressful life events were assessed in each subject. Furthermore, relationship between personality type of subjects (considering intensity of anxiety and the experience of stressful life events) with the means of recent four years averages(as an academic achievement indicator) was investigated. Data analysis by ANOVA in a computerized program • SPSS u indicated: 1) There are no significant differences in academic achievement in two personality types A and B . 2) Type A personality subjects, report significantly greater anxiety than type B personality subjects. 3) The experience of a stressful life events has a significant relationship to lower academic achievement . On the whole, results of this research, to some extent, are in accordance with other similar research.}, Keywords = {1) Tape A and B personality 2) Social achievement 3) Anxiety 4) Stressful events}, volume = {2}, Number = {0}, pages = {145-150}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1872-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1872-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Jalali, S.A.}, title = {REPORT OF SIX CASES OF LYNCH -1 SYNDROME}, abstract ={More than two decades ago, Henry T. Lynch reported a hereditary non polyposis colorectal cancer (HNPCC) which is seen in some families with dominant mode of inheritance, also know as Lynch Syndrome type I and II. This form to hereditary colorectal cancer has an early age of onset (Less than 45 years) with predominantly proximal colonic involvement (type I) and can also be associated with extracolonic cancer (type II). It is estimated that perhaps 4% - 13% of all cases of colorectal cancer are attributable to HNPCC. In this article, six cases of Cecal and / or ascending colon carcinoma are presented which are site-specific with a young age of onset, and one out of two of these patients are close relatives such as: brother and sister, mother and son and nephew and uncle, although for final Confirmation we need chromosome studies on these three families, but these could be considered clinically as Lynch 1- Syndrome pathology of most of these cases is of mucin-producing type adenocarcinoma. It is concluded that, because of a high incidence of colonic carcinoma with a young age of onset (perhaps around 50%) in Iran, the incidence of HNPCC could be much higher than in western populations.}, Keywords = {1) Lynch syndrome 2) Colon cancer 3) Adenocarcinoma}, volume = {2}, Number = {0}, pages = {5-10}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1873-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1873-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Hadjitarkhani, A.H.}, title = {IRANIAN MEDICAL JOURNALS}, abstract ={Remaining informed on the latest biochemical information is a necessity as well as a professional responsibility for any person involved in the field of medicine. The main and most readily available sources for updating the professional's knowledge are medical journals. In addition to foreign periodicals, there are a number of useful medical journals published in Iran. The first Persian language medical journal was published 90 years ago and throughout Iranian press history, the number of journals has varied during different Periods. Since 142 years ago when Iran first began its Publishing industry up to the victory of the Islamic Revolution medical periodicals have formed 3.4% of the total titles published, the oldest one being Issued 56 years ago In 1992, the number of Iranian medical periodicals was 31 (6.3% of total periodical titles), the majority of which is published by universities, government organizations and institutions and pharmaceutical companies. Of these titles, only three have International standard Serial Number (ISSN).}, Keywords = {1) Iranian medical journals 2) Health and Biomedical Information 3) Serials collection}, volume = {2}, Number = {0}, pages = {11-21}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1876-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1876-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Hariri, Mehrangiz and Eslami, Azar}, title = {SERIALS COLLECTION EVALUATION: A STRATEGY FOR CANCELLATIONS OR REINSTATEMENTS}, abstract ={}, Keywords = {1) Collection Development 2) Periodicals 3) Use frequency 4) Policies 5) Overlap}, volume = {2}, Number = {0}, pages = {22-29}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1877-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1877-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Roodpeyma, Shahl}, title = {ACUTE RESPIRATORY TRACT INFECTION IN CHILDREN}, abstract ={Acute Respiratory tract infections (ART!) are one of the most common problems encountered in childhood. In this article, epidemiology of ART! in the pediatric ward of Talegheni Medical center during a 5 year period from 1988 to 1993 was reviewed. 191 children were hospitalizid with ARTI. 184 (96.3%) suffered from LRT!, and of these, 150 patients had pneumonia (78.5%), 22 had Croups (11.5%), 12 had bronchiolitis (6.3%) and 7 Patients had Sinusitis (3.7%) . Children between 1 month to 1 year of age were the most common age group in patients with pneumonia and croup and accounted for 52. 7% of patients. In the same age group, in patients with pneumonia, there were 50 boys and 26 girls. The difference is statistically significant (p < 0.005). In patients with pneumonia and in those with croup MIF were ~ and 2.6 res                                                                                                                           1               1 pectively and winter was the most common season of affliction. In the bronchiolitis group both sexes were equal and half of the patients were hospitalized in spring and 41.6% in winter, 15.3% of patients with pneumonia did not receive antimicrobial treatment due to viral etiology and in the remainder (84.7%) antibactrial therapy was prescribed. Regarding the sex, age and seasonal pattern of respiratory tract infections, this study is compatible with the literature. Since the study was performed on hospitalized patients, the rate of bacterial pneumonia is higher than that reported in literature.}, Keywords = {1) Acute respiratory 2) Pneumonia 3) Croup 4) Bronchiolitis}, volume = {2}, Number = {0}, pages = {30-37}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1878-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1878-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Sadjadi, S.J. and Maleki, M. and Shamszadeh, A.}, title = {FLOWER POT CARRIER\'S SYNDROME (SADJADI - MALEKI SYNDROME)}, abstract ={Chest pain, especially in the left hemithorax, is a very common symptom, which often causes a patient to immediately seek medical advise, since it is often deemed to be related to cardiac diseeses. Some chest pains can be easily diagnosed and treated when a careful tilstory is taken and physical examination performed. One of the causes of chest pain which is common among housewives and some men is "flower pot carrier's syndrome' of 'sadjadi-maleki syndrome" which is being reported heve for the first time in medical literature In this syndrome, the patient's complain of upper chest pain which is aggrevated by change in position and teepirstory movements. Physical examination reveals tender zones. these patients often have a histoty of cartying Flower pots, cylinders and other things with chest support. In this syndrome, para clinic findings almost always are normal A ceretutnistory and physical examination can result in a definite diagnosis which will eliminate patient anxiety, save time and money wasted for unnecessary laboratory tests.}, Keywords = {1) Chest pain 2) Carrier pot 3) Tender zone}, volume = {2}, Number = {0}, pages = {38-43}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1879-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1879-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Shokohi, Hamid and Forghanizadeh, J. and Abhari, R. and Shakibi, M.R.}, title = {DEMOGRAPHIC DATA AND DIAGNOSIS OF 3856 PATIENTS ATTENDING THE RHEUMATIC DISEASES UNIT OF HAZRAT - E RASOOL HOSPITAL}, abstract ={OBJECTIVE: In order to determine demographic characteristics and to estimate the prevalence of various rheumatic diseases encountered in rheumatology clinic in Tehran, this survey was conducted. METHODS: This study was carry out at Hazzrat-e Rasool university hospital, the major teaching hospital of Iran university of medical sciences and health services. The study population consisted of 3856 consecutive newly refered patients of various ages who were seen at the clinic between May 1992 and June 1995. The patients were classified into diagnosis related groups (DRG) according to 1983 ARA classification of arthritis and rheumatism. RESUL TS: The 3856 studied patients had a mean age of 40 years and 67% were women. Connective tissue disease was the most common DRG which was found in 29.5% of the patients. Osteoarthritis and rheumatoid arthritis in various stages were the most common diseases found in 19.6% and 17.4% of the Patients respectively. Soft tissue rheumatism was found in 18.5%, infectious agents related rheumatic syndromes in 3%, Spondyloarthropathies in 3.8%, and nonspecific arthritis in 1.8% of the patients. No case of HIV related musculoskeletal problems was found in this survey. Erythema nodosum, carpal tunnel syndrome, fibromyalgia syndrome and  PSS were more common in women (F/M Ratio >8). and ankylosing spondylitis and gout in males (MIFRatio>8). Juvenile rheumatoid arthritis, acute rheumatic fever and vasculitis were the most common diseases in pediatrics patients (age of first visit« 16 years), and osteoarthritis (OA), rheumatoid arthritis (RA) and extraarticular lesions in geriatric patients (age of first vtsite: 60 years). RA (24.4%), SLE (11.6%), OA(10%) and vasculitis (6.5%) were the most common diseases in 525 hospitalized patients. SLE was the major cause of patient mortality. CONCLUSIONS: The results of this survey are compatible with data obtain from textbook and other similar surveys.}, Keywords = {1) Rheumatic disease 2) Rheumatic arthritis 3) Classification 4) Osteoarthritis}, volume = {2}, Number = {0}, pages = {44-52}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1880-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1880-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Fesharaki, M. and Hosseini, F. and Mohammadi-Nejad, G.A.}, title = {MAINTENANCE MANAGEMENT IN FIVE GENERAL HOSPITALS}, abstract ={Hospital maintenance and maintenance management is a new area which has recently been given more attention. It has special importance in developing countries where its economic aspects necessitates specific planning. In Iran, maintenance and problems associated with it have been considered to some extent in industry and related areas. However, it has not yet been given adequate attention in the health community, especially in hospitals. The present study was carried out to determine the maintenance conditions in five general hospitals during the year 1993-1994 with the use of descriptive method. The required information was collected through questionnaires and checklists. Due to inadequate accounting and financial records, we could not obtain exact figures concerning expenses in all these centers. Also, it was found that there were no experts for repairing and maintenance of medical and non-medical tools and equipment in aI/ five hospitals under study. Furthermore, none of the fol/owing areas has been taken into account in these hospitals: 1.   Maintenance training 2.   Maintenance committee 3.Instructions for controlling and checking the equipment before they are used. 4.    Written instructions for maintenance 5.   Personnel's responsibility in protecting and maintenance equipment 6.   Providing a file for maintenance of the hospital building and equipments.}, Keywords = {1) Maintenance 2) Maintenance training 3) Maintenance management}, volume = {2}, Number = {0}, pages = {53-61}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1881-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1881-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Ghoraeian, M.A.}, title = {THE EFFECTS OF PARATHYROIDECTOMY IN PATIENTS WITH RENAL OSTEODYSTROPHY}, abstract ={A known complication of chronic renal failure (CRF) is osteodystrophy. In order to determine the effects of parathyroidectomy on treatment and prevention of osteodystrophy progression in patients with CRF, a retrospective study was carried out in 16 hemodialysis patients. 62% of the patients underwent total, 12% subtotal and 26% total parathyroidectomy with simultaneous autograft in shahid Rahnamoon, hospital during 1983-1993. There was no recurrence of symptoms in any of the patients. Hypocalcemia was found in 40% and hypophosphatemia in 30% of the patients with total parathyroidectomy without autograft and in one of the cases who had subtotal parathyroidectomy. It is therefore concluded that total parathyroidectomy with autograft is superior to other conventional procedures, in the management of this complication}, Keywords = {1) Renal Osteodystrophy 2) Parathyroidectomy 3) CRF}, volume = {2}, Number = {0}, pages = {62-66}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1882-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1882-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Honarbakhsh, A. and Eatemadi, M. and Melekahmadi, B.}, title = {DETECTION OF FEFAL AGE WITH MEUSAREMENT OF FETAL BONE SCAPULA AT 13-35 WEEKS OF GESTATON AND COMPARISION WITH B.P.D}, abstract ={}, Keywords = {1) Scapula bone 2) Detection of fetal age 3) B.P.D}, volume = {2}, Number = {0}, pages = {67-76}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1883-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1883-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Akbarian, A.R. and Haghighi, L.}, title = {UPDATE ON UNEXPLAINED INFERTILITY}, abstract ={Unexplained infertility is considered when with application of standard investigations, including semen analysis, post coital test, endometrial biopsy, hysterosalpingography, and laparoscopy, etiologic factors are not found. With advances in science and technology and taking advantage of various assessment procedures especially during the last two decades, the prevalence of this entity is decreasing and at present it is about 10% . In this paper first the new diagnostic procedures such as sperm function tests, histochemical and immunohistochemical studies of endometrium, immunological studies and then various treatment methods including: ovarian hyperstimulation, intra uterine insemination, and intra fallopian gamete (zygote) transfer are described.}, Keywords = {1) Fertility 2) Infertility 3) Unexplained infertility(UEI) }, volume = {2}, Number = {0}, pages = {165-172}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1944-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1944-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Shemsadini, s.}, title = {KLEIN WAARDENBURG SYNDROME (KWS) A CASE REPORT}, abstract ={This is a case of 4-years-old white male who was referred to the dermatology clinic for two localised bald patches on parietal area noted 2 months previously. He was well naurished, well d.eveloped with fairly normal height and weight for his age, but with deafness, mutism, piebaldism, white forlock, paliosis of eye brows and eyelashes and musculoarticular abnormalities all noted from birth and early infancy. The association of these clinical findings are infavour of type 11/ waardenburg syndrome(klein type) , which is a rare disease. He is undergoing more investigation and evaluation.}, Keywords = {1)Klein waardenburg syndrome 2) White forlock 3) Allopecia 4) piebaldism }, volume = {2}, Number = {0}, pages = {173-176}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1946-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1946-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Amid, M.H.}, title = {LUMBAR PUNCTURE IN PATIENTS WITH FEBRILE CONVULSION}, abstract ={Meningitis in infants and children is an infectious disorder which has high mortality and morbidity. The disease present with different clinical manifestations and it may be present without signs of meningeal irritation, particularly in young infants. In this group, CNS infection may be present only with fever and seizure. On the other hand, one of the most. common and benign neurologic disorders during infancy and childhood is febrile convulsion which is not associated with any underlying disorder in CNS. Differential diagnosis between these two problems is difficult. Whether LP is indicated to rule out meningitis in infants with febrile convulsion is not clear. In a one year prospective study, CSF of children that presented with febrile convulsion with or without signs of meningitis, were examined. From 285 patients in whom LP was performed, 96(33.7%) of the cases had meningitis and 189(66.3 %) had normal CSF analysis. 61 cases (63.5%) were male and 35 cases(36.4%) were female, showing male predominance. In this study, from total patients, 124 children (43. 9%) presented only with fever and seizure, 18 cases (14.5%) of these patients had abnormal CSF.}, Keywords = {1)febrile convulsion 2) Seizure 3) Meningitis 4) Lumbar puncture }, volume = {2}, Number = {0}, pages = {177-181}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1948-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1948-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Forghanizadeh, j. and Abhari, R. and Shakibi, M.R. and Samadi, F. and Oiroozian, M. and Tavakoli, S.}, title = {PREVALENCE OF RHEUMATIC DISEASES IN FASHAM}, abstract ={The aim of this study is to determine the prevalence of rheumatic diseases in population aged 15 and over in Fasham-Shemiranat a mountainous rural area near Tehran, , The sampling method was house to house screening in villages of Fasham, Using the Community Oriented Program for Control 'of Rheumatic Diseases (COPCORD) core questionaire, 2502 persons were screened. In phase 1 , key questions concerned the presence of pain in neck dorsum, low back, sacrum and peripheral joints within the last 2 weeks or disabilities caused by pain in these regions or presence of pain in the past, lasting more than 6 weeks in these regions as well as questions regarding history of pain in great toes along with swelling or redness, subsiding within 2 weeks. Positive respondents for any of above questions entered phase 2 of the study which consisted of clinical examination, laboratory tests and X-ray studies. 1146 (45.8%) were negative cases in phase 1, Of 1358(54.2%) positive respondents, 282 (20.7%) no longer had complaints and therefore negative examinations. There were 251 (18.4%) drop_outs because of loss of follow up or lack of cooperation. In 825 cases (32.9%) one or more rheumatic conditions were diagnosed according to standard criteria. The prevalence of conditions was estimated as follows: Low back pain= 18.5% , Osteoarthritis (peripheral joints only) = 16.1%, Neck pain=6.4% , Periarthritis of snouider» 5%, other soft tissue conditions (tendinitis, elbow epicondylitis, carpal tunnel syndrome) =4.6%, Fibromyalgia= 1.3% , Rheumatoid arthritis = 0.32%, history of gouty attacks=0.28%, Psoriatic arthritis and Reiter's syndrome= 0.0£3010 . In conclusion, this study shows high prevalence of rheumatic conditions in a rural area with much higher prevalence rate of low back pain, osteoarthritis and other soft tissue conditions compared to low prevalence of inflammatory arthritis such es rheumatoid arthritis.}, Keywords = {1) Prevalence 2) Rheumatic disesases 3)Osteoarthritis 4)Soft tissue rheumatism 5) Rheumatoid arthritis }, volume = {2}, Number = {0}, pages = {182-191}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1949-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1949-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Mazhari, S.Z.}, title = {THE EFFECT OF VARIOUS FACTORS ON CLINICAL COURSE AND PRESENTATION OF PHENYLKETONURIA IN PATIENTS ADMITTED TO SHAHID AKBARABADI HOSPITAL}, abstract ={Phenylketonuria (PKU) is a hereditary metabolic disorder which is caused by complete or near complete deficiency of phenylalanin hydroxylase or other cofactors of the phenylalanin metabolic cycle. In this paper the data are collected from 312 patients who were referred to Shahid Akbarabadi Hospital . These patients were the result of 215 marriages which were familial in 192 instances. Most of these families referred to several specialists for diagnosis of the disease find from this point of view their socio-economic status had no effect. On the contrary, successful diet therapy and follow up Md close relation with socio-economic conditions. The high cost of special diet and medical care and emotional tension secondary to this disease in these children and their families are the major causes of the failure to control the disease. Divorce and addiction are the result of emotional tension in such families. Prohibiting familial marriage in those families with positive history is necessary for control and prevention of the disease.}, Keywords = {1) Phenyl ketonuria 2)Phenylalanin hydroxylase 3) Matrimony of Relatives }, volume = {2}, Number = {0}, pages = {192-199}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1950-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1950-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Nilforushan, M.A. and Hashemi, S. and Shokoohi, H.}, title = {EFFICACY ASSESSMENT OF NEONATAL B.C.G VACCINATION}, abstract ={BCG vaccine has been used since 1921 for primary prevention of tuberculosis in man. The immunogenic efficacy of this vaccine has been reported between 2 to 83/. in various studies. In order to assess the efficacy of neonatal BCG vaccination in 200 infants who had received BCG vecctne at birth, BCG vaccine scars were measured and PPD test (5 unit strength) was performed at 3 months of age. The survey was carried out from September 1993 to June 1994 in Shahid Akbarabad/ and Firoozgar University Hospitals. Positive BCG scars (defined, when ~ 3 mm in greater diameter) was present in 68/. of infants. PPD test results were negative « 5mm) in 321. , suspecious (5-9 mm) in 51/. and positive(~ 10mm) in 1T1. of cases. Proportion of positive PPD tests was higher in male (p<O.0005) and in positive BCG scar groups (p<0.005). There is a direct correlation between diameter of BCG scars and intensity of reaction to PPD tests. The most common complication of BCG vaccination was lymphadenitis which was detected in 2/. of infants.}, Keywords = {1) BCG vaccine 2) PPD test 3) BCGscar 4) Tuberculosis }, volume = {2}, Number = {0}, pages = {200-206}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1951-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1951-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} } @article{ author = {Honarbakhsh, A. and Iravani, B.}, title = {ULTRASOUND STUDY OF FETAL STOMACH}, abstract ={Ultrasound study of fetal stomach is multidirectionally rewarding . It can be used to detect congenital aberrations and to estimate gestational age in comparison with biparietal diamater (BPD). This study was performed in 60 pregnant women in 14-40 weeks of gestation. Maximum width and lengths of fetal stomach were measured and compared with BPD in order to determine gestational age . In 4 fetus, stomach was not visualized, This was caused by oligohydramnios in 2 and congenital neural tube defect in 1 case. Nonvisualization of fetal stomach after 14-20 weeks of gestation could be interpreted as indirect evidence of congenital abnormalities. In this study it was also noted that the measurements upleveled at 25th week of gestation resulting in the affecting parameters to intensify beyond this time. Ultrasound study was done only once without chronological repetition .}, Keywords = {1) Fetal stomach 2) Ultrasound 3) Biparietal diameter 4) Congenital abnormality }, volume = {2}, Number = {0}, pages = {207-210}, publisher = {Iran University of Medical Sciences}, url = {http://rjms.iums.ac.ir/article-1-1952-en.html}, eprint = {http://rjms.iums.ac.ir/article-1-1952-en.pdf}, journal = {Razi Journal of Medical Sciences}, issn = {2228-7043}, eissn = {2228-7051}, year = {1995} }